Thursday, March 6, 2008

What is infantile spasms syndrome?

The disease also known as the west syndrome, which is unique to baby during a seizure, the earlier the age of onset, has a special form of spastic, 90% with obvious intellectual and physical development disorders. Encephalitis, birth injuries, brain injury as a result of common diseases, men more than women, the incidence of time from a few days after birth to 30 months, with 3-nine of the majority, four-June for the summit. The clinical manifestations of the disease are the three major forms : (1) bow-like spasm : its performance to a sudden bout of short-term systemic muscle cramps, neck, trunk and legs bent, with admission or outreach, arms move outward embrace was extended emergency situation; (2) nod kind of spastic : There is a nod-like attack; (3) lightning-like spasm : very short duration, the attention is usually not difficult. Infantile Spasms attack performance five characteristics : (a) a single short time after the attack, an attack of two ~ 10 seconds; (2) total in particular the head and upper body forward flexion; (3) the number of frequent attacks, a day of multiple, each successive attack can be even dozens of times; (4) The attack is usually just fall asleep or sooner and the consciousness is still in a state of the cover, can be accompanied by loss of consciousness, sweating, Pikun facial bruising and lethargy; (5) ictal EEG were mixed. Attack interval is more characteristic of the peak dysrythmia. Of the disease in more than one-and-a-half of cessation, after the cessation of attacks, some evolved into other types of attacks, more than 90% of children with mental, retardation, hormone therapy to better effect.

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